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Pyridine metabolism in tea plants: salvage, conjugate formation and catabolism.
Journal of plant research 20121101
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m-Trifluoromethyl diphenyl diselenide attenuates glutaric acid-induced seizures and oxidative stress in rat pups: involvement of the γ-aminobutyric acidergic system.
Journal of neuroscience research 20120901
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Low-temperature phase transition in glycine-glutaric acid co-crystals studied by single-crystal X-ray diffraction, Raman spectroscopy and differential scanning calorimetry.
Acta crystallographica. Section B, Structural science 20120601
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Caspase-3 mediates apoptosis of striatal cells in GA I rat model.
Journal of Huazhong University of Science and Technology. Medical sciences = Hua zhong ke ji da xue xue bao. Yi xue Ying De wen ban = Huazhong keji daxue xuebao. Yixue Yingdewen ban 20120201
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Development of controlled release formulations of imidacloprid employing novel nano-ranged amphiphilic polymers.
Journal of environmental science and health. Part. B, Pesticides, food contaminants, and agricultural wastes 20120101
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Synthesis and in vitro evaluation of novel pro-drugs for the treatment of nephropathic cystinosis.
Bioorganic & medicinal chemistry 20110601
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Glutaric aciduria type 1 metabolites impair the succinate transport from astrocytic to neuronal cells.
The Journal of biological chemistry 20110520
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The sodium-dependent di- and tricarboxylate transporter, NaCT, is not responsible for the uptake of D-, L-2-hydroxyglutarate and 3-hydroxyglutarate into neurons.
Journal of inherited metabolic disease 20110401
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Clinical and molecular investigation of 19 Japanese cases of glutaric acidemia type 1.
Molecular genetics and metabolism 20110301
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Lipopolysaccharide enhances glutaric acid-induced seizure susceptibility in rat pups: behavioral and electroencephalographic approach.
Epilepsy research 20110201
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Synthesis, growth, crystal structure and characterization of a new organic material: glycine glutaric acid.
Spectrochimica acta. Part A, Molecular and biomolecular spectroscopy 20110101
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In vivo efficacy of dendrimer-methylprednisolone conjugate formulation for the treatment of lung inflammation.
International journal of pharmaceutics 20101031
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Studies of single aerosol particles containing malonic acid, glutaric acid, and their mixtures with sodium chloride. II. Liquid-state vapor pressures of the acids.
The journal of physical chemistry. A 20100923
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Glutaric aciduria type I and methylmalonic aciduria: simulation of cerebral import and export of accumulating neurotoxic dicarboxylic acids in in vitro models of the blood-brain barrier and the choroid plexus.
Biochimica et biophysica acta 20100601
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Induction of S100B secretion in C6 astroglial cells by the major metabolites accumulating in glutaric acidemia type I.
Metabolic brain disease 20100601
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Exploring rearrangements along the fragmentation of glutaric acid negative ion: a combined experimental and theoretical study.
Rapid communications in mass spectrometry : RCM 20100430
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Studies of single aerosol particles containing malonic acid, glutaric acid, and their mixtures with sodium chloride. I. Hygroscopic growth.
The journal of physical chemistry. A 20100429
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Compliance to clinical guidelines determines outcome in glutaric aciduria type I in the era of newborn screening.
Klinische Padiatrie 20100101
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Downstream processing of antibodies: single-stage versus multi-stage aqueous two-phase extraction.
Journal of chromatography. A 20091211
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Brain injury in glutaric aciduria type I: the value of functional techniques in magnetic resonance imaging.
European journal of paediatric neurology : EJPN : official journal of the European Paediatric Neurology Society 20091101
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Theoretical study of the nuO-H IR spectra for the hydrogen bond dimers from the polarized spectra of glutaric and 1-naphthoic acid crystals: Fermi resonances effects.
Spectrochimica acta. Part A, Molecular and biomolecular spectroscopy 20090915
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Modeling and prediction of cocrystal phase diagrams.
International journal of pharmaceutics 20090605
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Management of outpatient anesthesia in an unusually case with glutaric aciduria type-1.
Paediatric anaesthesia 20090601
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'Glutaric aciduria type I--an easily diagnosable and treatable metabolic disorder'.
Indian journal of pediatrics 20090501
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Glutaric aciduria type 1 presenting with epilepsy.
Developmental medicine and child neurology 20090301
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Kinetic characterization of l-[(3)H]glutamate uptake inhibition and increase oxidative damage induced by glutaric acid in striatal synaptosomes of rats.
International journal of developmental neuroscience : the official journal of the International Society for Developmental Neuroscience 20090201
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Disease-causing missense mutations affect enzymatic activity, stability and oligomerization of glutaryl-CoA dehydrogenase (GCDH).
Human molecular genetics 20081215
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Astrocytic proliferation and mitochondrial dysfunction induced by accumulated glutaric acidemia I (GAI) metabolites: possible implications for GAI pathogenesis.
Neurobiology of disease 20081201
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Genetic mapping of glutaric aciduria, type 3, to chromosome 7 and identification of mutations in c7orf10.
American journal of human genetics 20081117
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Target-driven selection in a dynamic nitrone library.
Chemical communications (Cambridge, England) 20080914
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Characterization of renal tubular apical efflux of zonampanel, an alpha-amino-3-hydroxy-5-methylisoxazole-4-propionate receptor antagonist, in humans.
Xenobiotica; the fate of foreign compounds in biological systems 20080901
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[Importance of early diagnosis and treatment in the prognosis of type I Glutaric Acidaemia].
Anales de pediatria (Barcelona, Spain : 2003) 20080901
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Newborn screening for glutaric aciduria type I in Victoria: treatment and outcome.
Molecular genetics and metabolism 20080701
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Prenatal cerebral ultrasound and MRI findings in glutaric aciduria Type 1: a de novo case.
Ultrasound in obstetrics & gynecology : the official journal of the International Society of Ultrasound in Obstetrics and Gynecology 20080601
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Gene symbol: GCDH. Disease: Glutaricacidaemia I.
Human genetics 20080601
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Development of a method for the quantification of D-glucaric acid in different varieties of grapefruits by high-performance liquid chromatography and mass spectra.
Journal of chromatography. A 20080509
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Outcome of three cases of untreated maternal glutaric aciduria type I.
European journal of pediatrics 20080501
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Maternal glutaric acidemia, type I identified by newborn screening.
Molecular genetics and metabolism 20080501
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Acquired multiple Acyl-CoA dehydrogenase deficiency in 10 horses with atypical myopathy.
Neuromuscular disorders : NMD 20080501
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Solid-state P-31 NMR study of the formation of hydroxyapatite in the presence of glutaric acid.
Magnetic resonance in chemistry : MRC 20080401
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Membrane translocation of glutaric acid and its derivatives.
Journal of inherited metabolic disease 20080401
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Chronic early postnatal glutaric acid administration causes cognitive deficits in the water maze.
Behavioural brain research 20080305
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Investigation of a wide spectrum of inherited metabolic disorders by 13C NMR spectroscopy.
Acta biochimica Polonica 20080101
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Creatine decreases convulsions and neurochemical alterations induced by glutaric acid in rats.
Brain research 20071214
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Evidence that glutaric acid reduces glutamate uptake by cerebral cortex of infant rats.
Life sciences 20071214
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Mechanism of age-dependent susceptibility and novel treatment strategy in glutaric acidemia type I.
The Journal of clinical investigation 20071101
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Evidence for a synergistic action of glutaric and 3-hydroxyglutaric acids disturbing rat brain energy metabolism.
International journal of developmental neuroscience : the official journal of the International Society for Developmental Neuroscience 20071001
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Biochemistry and bioenergetics of glutaryl-CoA dehydrogenase deficiency.
Journal of inherited metabolic disease 20071001
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Preparation and evaluation of chitosan/carrageenan beads for controlled release of sodium diclofenac.
AAPS PharmSciTech 20071001
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Age and brain structural related effects of glutaric and 3-hydroxyglutaric acids on glutamate binding to plasma membranes during rat brain development.
Cellular and molecular neurobiology 20070901
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[Glutaric aciduria type I with a low-excretion biochemical phenotype associated to a new mutation].
Revista de neurologia 20070701
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Induction of oxidative stress by chronic and acute glutaric acid administration to rats.
Cellular and molecular neurobiology 20070601
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[Type 1 glutaric aciduria: clinical and therapeutic implications].
Neurologia (Barcelona, Spain) 20070601
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Magnetic resonance imaging findings of adult-onset glutaric aciduria type I.
Acta radiologica (Stockholm, Sweden : 1987) 20070601
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Thermodynamic properties of malonic, succinic, and glutaric acids: evaporation rates and saturation vapor pressures.
Environmental science & technology 20070601
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Glutaric acid as a spacer facilitates improved intracellular uptake of LHRH-SPION into human breast cancer cells.
International journal of nanomedicine 20070601
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Covalent grafting of fibronectin onto plasma-treated PTFE: influence of the conjugation strategy on fibronectin biological activity.
Macromolecular bioscience 20070510
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[Glutaric aciduria type I. Clinical, biochemical and molecular findings in six patients in Venezuela].
Revista de neurologia 20070501
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Energy metabolism is compromised in skeletal muscle of rats chronically-treated with glutaric acid.
Metabolic brain disease 20070301
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Glutaric aciduria type 1 presenting as bilateral subdural hematomas mimicking nonaccidental trauma. Case report and review of the literature.
Journal of neurosurgery 20070301
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Determination of methylmalonic acid and glutaric acid in urine by aqueous-phase derivatization followed by headspace solid-phase microextraction and gas chromatography-mass spectrometry.
Journal of separation science 20070201
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The formation of byproducts in the autoxidation of cyclohexane.
Chemistry (Weinheim an der Bergstrasse, Germany) 20070101
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Heparan sulfate mediates neuroprotection from degeneration in experimental glutaric aciduria.
Cell transplantation 20070101
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Determination and modulation of prolyl-4-hydroxylase domain oxygen sensor activity.
Methods in enzymology 20070101
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[Neuroradiologic findings of glutaric aciduria type I].
Revista de medicina de la Universidad de Navarra 20070101
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Responses of ammonium sulfate particles coated with glutaric acid to cyclic changes in relative humidity: hygroscopicity and Raman characterization.
Environmental science & technology 20061115
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'So doctor, what exactly is wrong with my muscles? Glutaric aciduria type II presenting in a teenager'.
Neuromuscular disorders : NMD 20061001
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Magnetic resonance spectroscopic characteristics of glutaric aciduria type II.
Developmental medicine and child neurology 20061001
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[Type I glutaric aciduria: an unrecognized cause of progressive dystonia].
Revue neurologique 20060901
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Physical stability enhancement of theophylline via cocrystallization.
International journal of pharmaceutics 20060831
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Use of a glutaric acid cocrystal to improve oral bioavailability of a low solubility API.
Pharmaceutical research 20060801
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Lysine intake and neurotoxicity in glutaric aciduria type I: towards a rationale for therapy?
Brain : a journal of neurology 20060801
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New insights for glutaric aciduria type I.
Brain : a journal of neurology 20060801
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Investigations of the hygroscopic properties of ammonium sulfate and mixed ammonium sulfate and glutaric acid micro droplets by means of optical levitation and Raman spectroscopy.
Physical chemistry chemical physics : PCCP 20060621
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GM1 ganglioside prevents seizures, Na+,K+-ATPase activity inhibition and oxidative stress induced by glutaric acid and pentylenetetrazole.
Neurobiology of disease 20060601
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[A case report of glutaric acidemia].
Zhongguo dang dai er ke za zhi = Chinese journal of contemporary pediatrics 20060601
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Glutaric acidemia type 1.
American journal of medical genetics. Part C, Seminars in medical genetics 20060515
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Riboflavin-responsive glutaryl CoA dehydrogenase deficiency.
Molecular genetics and metabolism 20060501
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Glutaric acidemia type 1 in patients of Lumbee heritage from North Carolina.
Molecular genetics and metabolism 20060501
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Intracerebral accumulation of glutaric and 3-hydroxyglutaric acids secondary to limited flux across the blood-brain barrier constitute a biochemical risk factor for neurodegeneration in glutaryl-CoA dehydrogenase deficiency.
Journal of neurochemistry 20060501
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Glutaric aciduria types I and II.
Brain & development 20060401
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A diet-induced mouse model for glutaric aciduria type I.
Brain : a journal of neurology 20060401
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So doctor, what exactly is wrong with my muscles? Glutaric aciduria type II presenting in a teenager.
Neuromuscular disorders : NMD 20060401
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Efficient synthesis of trisimidazole and glutaric acid bearing porphyrins: ligands for active-site models of bacterial nitric oxide reductase.
Organic letters 20060302
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Transmembrane helices 3 and 4 are involved in substrate recognition by the Na+/dicarboxylate cotransporter, NaDC1.
Biochemistry 20060221
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Anesthetic management in two siblings with glutaric aciduria type 1.
Paediatric anaesthesia 20060201
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Endothelial effects of 3-hydroxyglutaric acid: implications for glutaric aciduria type I.
Pediatric research 20060201
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[L-2-hydroxyglutaric aciduria -- a rare cause of macrocephaly].
Klinische Padiatrie 20060101
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Breast feeding in organic acidaemias.
Journal of inherited metabolic disease 20060101
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Neonatal screening for glutaric aciduria type I: strategies to proceed.
Journal of inherited metabolic disease 20060101
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Rapid separation and analysis of six organic acids in Bayer liquors by RP-HPLC after solid-phase extraction.
Annali di chimica 20060101
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A preliminary in silico lead series of 2-phthalimidinoglutaric acid analogues designed as MMP-3 inhibitors.
Journal of chemical information and modeling 20060101
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Acidified acetonitrile and methanol extractions for quantitative analysis of acylcarnitines in plasma by stable isotope dilution tandem mass spectrometry.
Journal of chromatography. B, Analytical technologies in the biomedical and life sciences 20051205
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Glutaric acid moderately compromises energy metabolism in rat brain.
International journal of developmental neuroscience : the official journal of the International Society for Developmental Neuroscience 20051201
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Glutaryl-CoA dehydrogenase deficiency and newborn screening: retrospective analysis of a low excretor provides further evidence that some cases may be missed.
Molecular genetics and metabolism 20051101
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Conformations, energies, and intramolecular hydrogen bonds in dicarboxylic acids: implications for the design of synthetic dicarboxylic acid receptors.
Journal of computational chemistry 20050901
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Quantification of glutaric and 3-hydroxyglutaric acids in urine of glutaric acidemia type I patients by HPLC with intramolecular excimer-forming fluorescence derivatization.
Clinica chimica acta; international journal of clinical chemistry 20050901
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Glutaric acid administration impairs energy metabolism in midbrain and skeletal muscle of young rats.
Neurochemical research 20050901
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Prenatal diagnosis for organic acid disorders using two mass spectrometric methods, gas chromatography mass spectrometry and tandem mass spectrometry.
Journal of chromatography. B, Analytical technologies in the biomedical and life sciences 20050825
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Stable-isotope dilution gas chromatography-mass spectrometric measurement of 3-hydroxyglutaric acid, glutaric acid and related metabolites in body fluids of patients with glutaric aciduria type 1 found in newborn screening.
Journal of chromatography. B, Analytical technologies in the biomedical and life sciences 20050825
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Chemical modification of proteins during peroxidation of phospholipids.
Journal of lipid research 20050701
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Glutaric aciduria type I: a neuroimaging diagnosis?
Journal of child neurology 20050701
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Glutaric acid and its metabolites cause apoptosis in immature oligodendrocytes: a novel mechanism of white matter degeneration in glutaryl-CoA dehydrogenase deficiency.
Pediatric research 20050601
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Techniques to measure lipase and esterase activity in vitro.
Methods (San Diego, Calif.) 20050601
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[Macrocephaly the first manifestation of glutaric aciduria type I: the importance of early diagnosis].
Neurologia (Barcelona, Spain) 20050601
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[Glutaric aciduria type 1 with normal evolution: follow-up of one case until adult age].
Neurologia (Barcelona, Spain) 20050501
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[Application of tandem mass spectrometry in diagnosis of organic acidemias].
Zhonghua er ke za zhi = Chinese journal of pediatrics 20050501
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Neuropathological, biochemical and molecular findings in a glutaric acidemia type 1 cohort.
Brain : a journal of neurology 20050401
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Glutaric aciduria type 1: a clinician's view of progress.
Brain : a journal of neurology 20050401
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Structure of Escherichia coli glutamate decarboxylase (GADalpha) in complex with glutarate at 2.05 angstroms resolution.
Acta crystallographica. Section D, Biological crystallography 20050301
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Diffusion-weighted MR imaging and MR spectroscopy in glutaric aciduria type 1.
Neuroradiology 20050301
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The urinary excretion of glutarylcarnitine is an informative tool in the biochemical diagnosis of glutaric acidemia type I.
Molecular genetics and metabolism 20050201
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Breastfeeding experience in inborn errors of metabolism other than phenylketonuria.
Journal of inherited metabolic disease 20050101
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Glutaric aciduria type II: a case report.
International journal of immunopathology and pharmacology 20050101
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Glutaric acid stimulates glutamate binding and astrocytic uptake and inhibits vesicular glutamate uptake in forebrain from young rats.
Neurochemistry international 20041201
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[In utero macrocephaly as clinical manifestation of glutaric aciduria type I. Report of a novel mutation].
Revista de neurologia 20041101
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Brief report: Predictors of parenting stress among parents of children with biochemical genetic disorders.
Journal of pediatric psychology 20041001
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Glutaric aciduria type I associated with learning disability.
Indian journal of pediatrics 20041001
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Riboflavin-responsive glutaric aciduria type II with recurrent pancreatitis.
Pediatric neurology 20040901
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Glutaric aciduria type 1: proton magnetic resonance spectroscopy findings.
Pediatric neurology 20040901
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Low molecular weight dicarboxylic acids in PM10 in a city with intensive solid fuel burning.
Chemosphere 20040801
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On the neurotoxicity of glutaric, 3-hydroxyglutaric, and trans-glutaconic acids in glutaric acidemia type 1.
Journal of neuroscience research 20040701
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Genetic and biochemical study in a patient with glutaric acidemia type I.
Journal of the Formosan Medical Association = Taiwan yi zhi 20040701
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[Glutaric aciduria type I: report of a case].
Zhonghua er ke za zhi = Chinese journal of pediatrics 20040701
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D-2-hydroxyglutaric aciduria and glutaric aciduria type 1 in siblings: coincidence, or linked disorders?
Neuropediatrics 20040601
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Solvent-drop grinding: green polymorph control of cocrystallisation.
Chemical communications (Cambridge, England) 20040407
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Pathomechanisms of neurodegeneration in glutaryl-CoA dehydrogenase deficiency.
Annals of neurology 20040101
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Glutaric aciduria type I: value of diffusion-weighted magnetic resonance imaging for diagnosing acute striatal necrosis.
Journal of computer assisted tomography 20040101
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Long-term follow-up, neurological outcome and survival rate in 28 Nordic patients with glutaric aciduria type 1.
European journal of paediatric neurology : EJPN : official journal of the European Paediatric Neurology Society 20040101
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Bilateral pallidotomy for severe dystonia in an 18-month-old child with glutaric aciduria.
Stereotactic and functional neurosurgery 20040101
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[Application of bisalkaloid derivatives of dicarboxylic acids based on lupinine, anabasine and cytisine as cholinesterase inhibitors of various origin].
Zhurnal evoliutsionnoi biokhimii i fiziologii 20040101
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Development of pathogenic concepts in glutaryl-CoA dehydrogenase deficiency: the challenge.
Journal of inherited metabolic disease 20040101
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Animal models for glutaryl-CoA dehydrogenase deficiency.
Journal of inherited metabolic disease 20040101
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Preliminary attempts to establish a rat model of striatal injury in glutaric acidaemia type I.
Journal of inherited metabolic disease 20040101
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Vascular dysfunction as an additional pathomechanism in glutaric aciduria type I.
Journal of inherited metabolic disease 20040101
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Glutaric aciduria type I and kynurenine pathway metabolites: a modified hypothesis.
Journal of inherited metabolic disease 20040101
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Challenges for basic research in glutaryl-CoA dehydrogenase deficiency.
Journal of inherited metabolic disease 20040101
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Correlation of genotype and phenotype in glutaryl-CoA dehydrogenase deficiency.
Journal of inherited metabolic disease 20040101
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Neuroradiological findings in glutaric aciduria type I (glutaryl-CoA dehydrogenase deficiency).
Journal of inherited metabolic disease 20040101
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Glutaric aciduria type I: outcome in the Republic of Ireland.
Journal of inherited metabolic disease 20040101
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Glutaric aciduria type 1 in a Kuwaiti infant.
Eastern Mediterranean health journal = La revue de sante de la Mediterranee orientale = al-Majallah al-sihhiyah li-sharq al-mutawassit 20040101
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Glutaric aciduria type 1 and neonatal screening: time to proceed--with caution.
European journal of pediatrics 20031201
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[Late-onset riboflavin-responsive multiple acyl-CoA dehydrogenase deficiency (glutaric aciduria type II)].
Zhonghua er ke za zhi = Chinese journal of pediatrics 20031201
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Induction of oxidative stress by L-2-hydroxyglutaric acid in rat brain.
Journal of neuroscience research 20031001
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Intraretinal hemorrhages and chronic subdural effusions: glutaric aciduria type 1 can be mistaken for shaken baby syndrome.
Retina (Philadelphia, Pa.) 20031001
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Type I glutaric aciduria: phenotypes and genotypes in 5 Taiwanese children.
Journal of the Formosan Medical Association = Taiwan yi zhi 20031001
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Studies into the thermodynamic origin of negative cooperativity in ion-pairing molecular recognition.
Journal of the American Chemical Society 20030910
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Human mutation 20030701
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[Vegetarian diet in glutaric aciduria type I].
Anales de pediatria (Barcelona, Spain : 2003) 20030701
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Investigation of surface changes of nanoparticles using TM-AFM phase imaging.
Environmental science & technology 20030615
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Capillary electrophoresis for the determination of organic acidurias in body fluids: a review.
Clinical chemistry and laboratory medicine 20030601
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Glutaryl-CoA dehydrogenase deficiency: region-specific analysis of organic acids and acylcarnitines in post mortem brain predicts vulnerability of the putamen.
Neuropediatrics 20030601
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Adult onset glutaric aciduria type I presenting with a leukoencephalopathy.
Neurology 20030422
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Organic anion transporter 3 (Slc22a8) is a dicarboxylate exchanger indirectly coupled to the Na+ gradient.
American journal of physiology. Renal physiology 20030401
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Late-onset form of beta-electron transfer flavoprotein deficiency.
Molecular genetics and metabolism 20030401
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Spondyloenchondromatosis with D-2-hydroxyglutaric aciduria: a report of a second patient with this unusual combination.
Clinical dysmorphology 20030401
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Glutaric acid induces oxidative stress in brain of young rats.
Brain research 20030221
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Glutaric aciduria I: creatine supplementation restores creatinephosphate levels in mixed cortex cells from rat incubated with 3-hydroxyglutarate.
Molecular genetics and metabolism 20030201
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Neurological toxicity of ifosfamide.
Oncology 20030101
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Rhabdomyolysis in glutaric aciduria type I.
Journal of inherited metabolic disease 20030101
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Severe phenotype despite high residual glutaryl-CoA dehydrogenase activity: a novel mutation in a Turkish patient with glutaric aciduria type I.
Journal of inherited metabolic disease 20030101
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[Glutaric aciduria type 1: an example of the importance of early detection of so-called cerebral organic aciduria].
Lijecnicki vjesnik 20030101
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Adult onset glutaric aciduria type I presenting with a leukoencephalopathy.
Neurology 20021210
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Antitumor activities of conjugates of mitomycin C with estradiol benzoate and estradiol via glutaric acid in suspension dosage form.
Biological & pharmaceutical bulletin 20021001
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Glutaric aciduria type III: a distinctive non-disease?
Journal of inherited metabolic disease 20021001
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Novel mutation and prenatal sonographic findings of glutaric aciduria (type I) in two Taiwanese families.
Prenatal diagnosis 20020801
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NMDA receptor activation and respiratory chain complex V inhibition contribute to neurodegeneration in d-2-hydroxyglutaric aciduria.
The European journal of neuroscience 20020701
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Chronic treatment with glutaric acid induces partial tolerance to excitotoxicity in neuronal cultures from chick embryo telencephalons.
Journal of neuroscience research 20020515
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Glutaric aciduria type I diagnosed after poliovirus immunization: magnetic resonance findings.
Pediatric neurology 20020501
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Nihon rinsho. Japanese journal of clinical medicine 20020401
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[Glutaric aciduria type 2].
Nihon rinsho. Japanese journal of clinical medicine 20020401
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Glutaric aciduria type 1 and nonaccidental head injury.
Pediatrics 20020301
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Synthesis, pharmacokinetics, efficacy, and rat retinal toxicity of a novel mitomycin C-triamcinolone acetonide conjugate.
Journal of medicinal chemistry 20020227
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Biochemical, pathologic and behavioral analysis of a mouse model of glutaric acidemia type I.
Human molecular genetics 20020215
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A 9-month-old baby with subdural hematomas, retinal hemorrhages, and developmental delay.
Pediatric emergency care 20020201
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Outcome of the first 3-years of a DNA-based neonatal screening program for glutaric acidemia type 1 in Manitoba and northwestern Ontario, Canada.
Molecular genetics and metabolism 20020101
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Glutaric acidemia type II: gene structure and mutations of the electron transfer flavoprotein:ubiquinone oxidoreductase (ETF:QO) gene.
Molecular genetics and metabolism 20020101
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[Organic acid disorders: cerebral organic acidemia].
Ryoikibetsu shokogun shirizu 20020101
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Allosteric behaviour of 1:5 hybrids of mutant subunits of Clostridium symbiosum glutamate dehydrogenase differing in their amino acid specificity.
The Biochemical journal 20011215
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Mechanisms of brain injury in infantile child abuse.
Lancet (London, England) 20011215
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X-ray studies on crystalline complexes involving amino acids and peptides. XXXVIII. Crystal structures of the complexes of L-arginine and L-histidine with glutaric acid and a comparative study of amino acid-glutaric acid complexes.
Acta crystallographica. Section B, Structural science 20011201
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Prenatal diagnosis of glutaric acidemias.
Prenatal diagnosis 20011201
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Biochemical and molecular diagnosis of glutaric aciduria type 1 in a black South African male child: case report.
East African medical journal 20011201
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Journal of inherited metabolic disease 20011101
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Indian pediatrics 20011001
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Neurologia (Barcelona, Spain) 20011001
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Neurologia (Barcelona, Spain) 20011001
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A Korean girl with alpha-aminoadipic and alpha-ketoadipic aciduria accompanied with elevation of 2-hydroxyglutarate and glutarate.
Journal of inherited metabolic disease 20010801
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L-2-Hydroxyglutaric aciduria presenting as status epilepticus.
Brain & development 20010701
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Revista de neurologia 20010701
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X-ray studies on crystalline complexes involving amino acids and peptides. XXXVII. Novel aggregation patterns and effect of chirality in the complexes of DL- and L-lysine with glutaric acid.
Acta crystallographica. Section B, Structural science 20010601
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High-resolution (1)H NMR and magic angle spinning NMR spectroscopic investigation of the biochemical effects of 2-bromoethanamine in intact renal and hepatic tissue.
Magnetic resonance in medicine 20010501
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Glutaric acidemia, type I, missed by newborn screening in an infant with dystonia following promethazine administration.
Pediatrics 20010501
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Pediatrics 20010201
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Glutaric aciduria type 1 and nonaccidental head injury.
Pediatrics 20010101
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[Hyperthyroidism in early childhood and a very rare variant of glutaric aciduria: coincidence or causal relation?].
Klinische Padiatrie 20010101
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Metal-assisted esterification: glutaric acid-iron(II) complexes in the gas phase.
Rapid communications in mass spectrometry : RCM 20010101
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Acrodermatitis acidemica secondary to malnutrition in glutaric aciduria type I.
European journal of dermatology : EJD 20010101
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The effect of surfactants on the deliquescence of sodium chloride.
Journal of environmental science and health. Part A, Toxic/hazardous substances & environmental engineering 20010101
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[Aciduria, glutaric (type 1)].
Ryoikibetsu shokogun shirizu 20010101
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Ryoikibetsu shokogun shirizu 20010101
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Subdural haematoma, non-accidental head injury or ...?
European journal of paediatric neurology : EJPN : official journal of the European Paediatric Neurology Society 20010101
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[Glutaric aciduria type 2].
Ryoikibetsu shokogun shirizu 20010101
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Pediatric research 20000401
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Elucidation of the complete Azorhizobium nicotinate catabolism pathway.
Journal of bacteriology 19921201
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The Journal of biological chemistry 19621101